Solitary Radiolucent Erdheim-chester Disease: A Case Report and Literature Review
Aleksandar Popovic1, Christopher Curtiss2, Timothy A. Damron3, *
Identifiers and Pagination:Year: 2021
First Page: 77
Last Page: 82
Publisher ID: TOORTHJ-15-77
Article History:Received Date: 18/3/2021
Revision Received Date: 8/10/2021
Acceptance Date: 29/10/2021
Electronic publication date: 31/12/2021
Collection year: 2021
open-access license: This is an open access article distributed under the terms of the Creative Commons Attribution 4.0 International Public License (CC-BY 4.0), a copy of which is available at: https://creativecommons.org/licenses/by/4.0/legalcode. This license permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
Erdheim-chester disease (ECD) is a rare non-Langerhans histiocytosis of unknown etiology, which typically presents with bilateral symmetric osteosclerosis and multi-organ involvement. Lesions may be intraosseous or extraosseous and involve the heart, pulmonary system, CNS, and skin in order of decreasing likelihood.
The objective of this study is to discuss a case of erdheim-chester disease and conduct a review of the literature.
We describe a rare case of erdheim-chester in an asymptomatic 37-year-old male who was diagnosed after suffering a right ulnar injury. Subsequent evaluation revealed a solitary radiolucent ulnar lesion without multi-system involvement.
Results & Conclusion:
The case is unique in its solitary distribution, lytic radiographic appearance, and asymptomatic presentation preceding pathologic fracture. This presentation may simulate multiple other bone lesions.